ABSTRACT
Background: Inflammatory pseudo tumor, a rare non-neoplastic lesion, commonlypresents as slow growing solid lesion in the lung, but many extra-pulmonary locations havebeen described. Case characteristics: A 4-year-old girl who presented with respiratorydistress due to massive pleural effusion. Computed tomography revealed large hypodensenon-enhancing lesion in the left hemi thorax. Surgical exploration revealed large semisolidpleural collection filled with gelatinous material with normal underlying lung. Outcome:Histopathology revealed spindle shaped cells with abundant myxoid stroma. Childrecovered after surgery and was asymptomatic at 5 years follow-up. Message: Primarypleural inflammatory pseudotumor may be a rare cause of pleural effusion in a child